Successful resection of esophageal carcinosarcoma in presence of right aortic arch: A case report

Zhong-Xi Niu, Yao Chen, Jun Peng, Hui Shi, Long-Qi Chen


We herein report a giant esophageal carcinosarcoma (ECS) occupying the entire intrathoracic esophagus with a coexisting right aortic arch (RAA). The patient was admitted with severe dysphagia and weight loss. Subtotal esophagectomy was performed via left thoraco-cervical approach with cervical esophagogastric anastomosis. The aortopulmonary ligament was ligated and dissected at first for better exposure. Patient recovered uneventfully and there was no evidence of recurrence during the 1 year follow-up period. To our knowledge, this is the first report of such a giant ECS with coexisting RAA. For this kind of patient, a left thoracotomy approach and cervical anastomosis is recommended, and the dissection of aortopulmonary ligament is usually required.

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